Resumen
What is Idiopathic Pulmonary Fibrosis
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive lung disease characterized by progressive lung scarring and the histological picture of usual interstitial pneumonia (UIP). IPF is the most common and most lethal type of interstitial lung disease (ILD).
How common is Idiopathic Pulmonary Fibrosis
The estimated prevalence of IPF in the United States varies between 14 and 27,9 cases per 100.000 of the population, while incidence of IPF in the U.S. is estimated at 6,8 to 8,8 cases per 100.000.1 IPF is diagnosed more commonly in men vs. women and most commonly diagnosed in patients age 75 or older. Idiopathic Pulmonary Fibrosis newly occurs in approximately 12 per 100.000 people per year.
Questions regarding your Idiopathic Pulmonary Fibrosis therapy
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- 1Luba Nalysnyk, Javier Cid-Ruzafa, Philip Rotella, Dirk Esser. European Respiratory Review Dec 2012, 21 (126) 355-361; DOI: 10,1183/09059180,00002512
Síntomas
What are the symptoms of Idiopathic Pulmonary Fibrosis
Symptoms of IPF may include:
- Exertional dyspnea
- Labored breathing
- Tos seca
- Muscle and joint aches
- Falta de energía (también llamada fatiga)
- Pérdida del apetito
- pérdida de peso
- Clubbing (rounding of the tips of the fingers or toes)
Cómo se diagnostica
The diagnosis of idiopathic pulmonary fibrosis can be challenging. Signs and symptoms can be very similar to other interstitial lung disease disorders. Additionally, other disease states can display signs and symptoms similar to IPF, therefore ruling out other disorders is essential before making a diagnosis.
Análisis de sangre
Blood tests can detect oxygen or carbon dioxide level abnormalities that could assist in the diagnosis of IPF.
Diagnóstico por imágenes
A chest radiograph (X-ray) can be used to assist in the diagnosis, although it is not diagnostic on its own. Chest radiographs are low sensitivity and would show lower lobe volume loss in more advanced disease states. A High-resolution computed tomography (HRCT) is the gold standard for IPF diagnosis. It has excellent specificity and can diagnosis IPF through the presence of “honeycombing” patterns in the lungs.
Pruebas de la función pulmonar
Estas pruebas miden cuánto aire pueden contener sus pulmones, cuánto aire ingresa y sale de sus pulmones, y la capacidad de los pulmones de intercambiar oxígeno. Estas pruebas pueden realizarse para identificar potencialmente la causa. Specific pulmonary function tests include Spirometry and diffusion capacity and Oximetry.
Lung tissue analysis
Tissue samples of a patient’s lung can be helpful in determining diagnosis of idiopathic pulmonary fibrosis. Bronchoscopy, bronchoalveolar lavage, and surgical biopsy are particular ways in which tissue samples can be collected.
High resolution computerized tomography
This imaging test is key to, and sometimes the first step in, the diagnosis of idiopathic pulmonary fibrosis. CT scanners use a computer to combine X-ray images taken from many different angles to produce cross-sectional images of internal structures. A high-resolution CT scan can be particularly helpful in determining the extent of lung damage caused by IPF. It can show details of the fibrosis, which can be helpful in narrowing down the diagnosis of IPF, which is characterized as a “honeycombing” pattern.
Medicamentos
Idiopathic Pulmonary Fibrosis (IPF) Medications
While there is currently no cure for IPF, different treatment options are available to help you manage your disease and feel better day-to-day. Your doctor may prescribe other medication(s) as part of your treatment based on your particular symptoms and level of severity. The following specialty medication is available at Accredo for the treatment of IPF.
Financiación de su atención
Es posible que haya coordinación de asistencia financiera disponible para ayudar con los costos de sus medicamentos, incluidos programas de los fabricantes y programas comunitarios. Los representantes de Accredo están disponibles para ayudarlo a encontrar un programa que funcione para usted.
Recursos económicos comunitarios
- PSI-Patient Services, Inc. | 800-366-7741
- Fundación para la Defensa del Paciente (Patient Advocate Foundation) | 800-532-5274
- El Fondo de Asistencia (The Assistance Fund) | 855-845-3663
- Fundación Healthwell (Healthwell Foundation) | 800- 675-8416
- Esbriet® (pirfenidone) Financial Assistance & Copay Information | 844-693-7274
- Ofev® (nintedanib) Capsules Financial Assistance Information | 855-297-5906
Orientación financiera
Los medicamentos de especialidad que salvan vidas pueden ser costosos. Conozca en este video cómo los equipos Accredo ayudan a las personas a encontrar formas de costear el medicamento que necesitan para sobrevivir.
Encuentre apoyo
There are organizations that support research and advocacy for pulmonary fibrosis. Consulte a continuación algunas de estas organizaciones.
Organizaciones de apoyo
- Pulmonary Fibrosis Foundation
- Instituto Nacional del Corazón, los Pulmones y la Sangre (National Heart, Lung, and Blood Institute, NHLBI)
- Organización Nacional de Trastornos Poco Frecuentes (National Organization of Rare Disorders, NORD)
Organizaciones gubernamentales
Conozca al equipo
Accredo’s Idiopathic pulmonary fibrosis care team is dedicated to serving you and we understand the complexity of your condition. Nuestros médicos clínicos con formación especializada están disponibles las 24 horas al día, los siete días de la semana, para responder cualquier pregunta.
Por qué lo hacemos
Accredo brinda apoyo a pacientes con afecciones crónicas y complejas, y los ayuda a vivir mejor su vida. Mire nuestro video para conocer por qué hacemos lo que hacemos por nuestros pacientes.